pyropoikilocytosis

pyropoikilocytosis
A rare recessive disorder manifested by severe hemolysis, marked poikilocytosis, and a characteristic sensitivity of the red cells to heat-induced fragmentation in vitro; apparently due to a defect in spectrin self-association. SYN: hereditary p..
- hereditary p. SYN: p..

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py·ro·poi·ki·lo·cy·to·sis (pi″ro-poi″kĭ-lo-si-toґsis) presence in the blood of numerous bizarre-shaped heat-sensitive poikilocytes.

Medical dictionary. 2011.

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