erythrokeratodermia variabilis

erythrokeratodermia variabilis
a rare autosomal dominant condition present at birth, characterized by both transient, migratory areas of erythroderma in various shapes and fixed plaques of hyperkeratosis. Called also keratoderma palmoplantare transgrediens and keratosis palmoplantaris transgrediens.

Medical dictionary. 2011.

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