purine-nucleoside phosphorylase

purine-nucleoside phosphorylase
pu·rine-nu·cleo·side phos·phor·y·lase (puґrēn nooґkle-o-sīd fos-forґə-lās) [EC 2.4.2.1] an enzyme of the transferase class that catalyzes the cleavage of purine nucleosides to form purines and ribose 1-phosphates in the degradation of nucleotides and nucleic acids. Absence of activity, an autosomal recessive trait, results in defective cell-mediated immunity.

Medical dictionary. 2011.

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  • purine nucleoside phosphorylase — purine nucleoside phosphorylase, an enzyme that keeps T cells functioning by cleansing them of contaminants: »Purine nucleoside phosphorylase…cleans up metabolic debris that would otherwise build up inside the T cells and shut them down (Jane E.… …   Useful english dictionary

  • purine nucleoside phosphorylase — purine nucleoside phosphorylase. См. пурин нуклеозидфосфорилаза. (Источник: «Англо русский толковый словарь генетических терминов». Арефьев В.А., Лисовенко Л.А., Москва: Изд во ВНИРО, 1995 г.) …   Молекулярная биология и генетика. Толковый словарь.

  • Purine nucleoside phosphorylase — Not to be confused with polynucleotide phosphorylase. purine nucleoside phosphorylase Identifiers EC number 2.4.2.1 CAS number …   Wikipedia

  • Purine-nucleoside phosphorylase — In enzymology, a purine nucleoside phosphorylase (EC number|2.4.2.1) is an enzyme that catalyzes the chemical reaction:purine nucleoside + phosphate ightleftharpoons purine + alpha D ribose 1 phosphateThus, the two substrates of this enzyme are… …   Wikipedia

  • Purine nucleoside phosphorylase deficiency — Infobox Disease Name = PAGENAME Caption = DiseasesDB = 11044 ICD10 = ICD10|D|81|5|d|80 ICD9 = ICD9|277.2 ICDO = OMIM = 164050 MedlinePlus = eMedicineSubj = ped eMedicineTopic = 1957 MeshID = Purine nucleoside phosphorylase deficiency, often… …   Wikipedia

  • Deficit en purine nucleoside phosphorylase — Déficit en purine nucléoside phosphorylase Le déficit en purine nucléoside phosphorylase entre dans le cadre d un déficit immunitaire congénital. Il existe un déficit de l immunité cellulaire et une anomalie de production de certains anticorps.… …   Wikipédia en Français

  • Déficit En Purine Nucléoside Phosphorylase — Le déficit en purine nucléoside phosphorylase entre dans le cadre d un déficit immunitaire congénital. Il existe un déficit de l immunité cellulaire et une anomalie de production de certains anticorps. Sa transmission est autosomique dominante.… …   Wikipédia en Français

  • Déficit en purine nucléoside phosphorylase — Le déficit en purine nucléoside phosphorylase entre dans le cadre d un déficit immunitaire congénital. Il existe un déficit de l immunité cellulaire et une anomalie de production de certains anticorps. Sa transmission est autosomique dominante.… …   Wikipédia en Français

  • Nucleoside phosphorylase — Nucleoside phosphorylase, also known as NP, is a human gene.cite web | title = Entrez Gene: NP nucleoside phosphorylase| url = http://www.ncbi.nlm.nih.gov/sites/entrez?Db=gene Cmd=ShowDetailView TermToSearch=4860| accessdate = ] PBB Summary… …   Wikipedia

  • nucleoside phosphorylase — n NUCLEOSIDASE (2) * * * nu·cleo·side phos·phor·y·lase (nooґkle o sīd″ fos forґə lās) any of the enzymes of the sub subclass pentosyltransferases [EC 2.4.2] that catalyze the phosphorolysis of a nucleoside to form the free… …   Medical dictionary

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