pachydermoperiostosis


pachydermoperiostosis
A syndrome of clubbing of the digits, periosteal new bone formation, especially over the distal ends of the long bones (idiopathic hypertrophic osteoarthropathy), and coarsening of the facial features with thickening, furrowing, and oiliness of the skin of the face and forehead (cutis verticis gyrata); there is seborrheic hyperplasia with open sebaceous pores filled with plugs of sebum; often of autosomal dominant inheritance, usually more severe in males. SYN: acropachyderma. [pachy- + G. derma, skin, + periostosis]

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pachy·der·mo·peri·os·to·sis (pak″e-dur″mo-per″e-os-toґsis) [pachy- + dermo- + periostosis] a rare syndrome characterized by pachyderma with deep folds and furrows on the forehead, cheeks, and scalp (cutis verticis gyrata), as well as seborrhea, hyperhidrosis, periostosis of long bones, digital clubbing, and spadelike enlargement of the hands and feet. It is more prevalent in males and usually first appears during adolescence. Some forms are hereditary and others are secondary to cardiopulmonary diseases or malignancies. Called also idiopathic or primary hypertrophic osteoarthropathy and Touraine-Solente-Golй syndrome.

Medical dictionary. 2011.

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  • Pachydermoperiostosis — Infobox Disease Name = PAGENAME Caption = DiseasesDB = 29069 ICD10 = ICD10|L|62|0|l|60, ICD10|M|89|4|m|86 ICD9 = ICD9|731.2, ICD9|757.39 ICDO = OMIM = 167100 MedlinePlus = eMedicineSubj = derm eMedicineTopic = 815 MeshID = D010004… …   Wikipedia

  • acropachyderma with pachyperiostitis — pachydermoperiostosis …   Medical dictionary

  • Touraine-Solente-Golй syndrome — pachydermoperiostosis …   Medical dictionary

  • Primary hypertrophic osteoathropathy — Pachydermoperiostosis Classification and external resources ICD 10 L62.0, M89.4 ICD 9 …   Wikipedia

  • пахидермопериостоз — (pachydermoperiostosis; пахи греч. derma кожа + анат. periosteum надкостница + оз; син. Турена Соланта Голе синдром) наследственная болезнь, проявляющаяся сочетанием кератодермии, пахидермии лица и гиперплазии сальных желез с билатеральным… …   Большой медицинский словарь

  • Pachyderma — Infobox Disease Name = PAGENAME Caption = DiseasesDB = ICD10 = ICD9 = ICD9|701.8 ICDO = OMIM = MedlinePlus = eMedicineSubj = eMedicineTopic = MeshID = Pachyderma is the thickening of skin like that of a pachyderm. [cite web |url=… …   Wikipedia

  • Пахидермопериостоз — I Пахидермопериостоз (pachydermoperiostosis; греч. pachys толстый, плотный + derma кожа + анат. periosteum надкостница + ōsis: синоним: синдром Турена Соланта Голе, идиопатическая гипертрофическая остеоартропатия) наследственная форма… …   Медицинская энциклопедия

  • syndrome — The aggregate of symptoms and signs associated with any morbid process, and constituting together the picture of the disease. SEE ALSO: disease. [G. s., a running together, tumultuous concourse; (in med.) a concurrence of symptoms, fr. syn,… …   Medical dictionary

  • List of diseases (P) — A list of diseases in the English Wikipedia.DiseasesTOC PaPac Pal* Pachydermoperiostosis * Pachygyria * Pachyonychia congenita Jackson Lawler type * Pacman dysplasia * Paes Whelan Modi syndrome * Paget disease extramammary * Paget disease… …   Wikipedia

  • Liste der Syndrome — Diese Seite listet in alphabetischer Reihenfolge und ohne Anspruch auf Vollständigkeit Syndrome und Komplexe aus unterschiedlichen medizinischen Fachgebieten auf. Bitte nur Verweise auf den tatsächlichen Titel des Beitrags und keine… …   Deutsch Wikipedia