proteinosis


proteinosis
A state characterized by disordered protein formation and distribution, particularly as manifested by the deposition of abnormal proteins in tissues. [protein + G. -osis, condition]
- lipoid p. [MIM*247100] a disturbance of lipid metabolism in which there are deposits of a protein-lipid complex on the tongue and sublingual and faucial areas leading to hoarseness, and translucent keratotic papillomatous eyelid lesions; autosomal recessive inheritance, frequently with specific intracranial calcifications. SYN: hyalinosis cutis et mucosae, lipoidosis cutis et mucosae, Urbach-Wiethe disease.
- pulmonary alveolar p. a chronic progressive lung disease of adults, characterized by alveolar accumulation of granular proteinaceous material that is PAS-positive and lipid- rich, with little inflammatory cellular exudate; the cause is unknown.

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pro·tein·o·sis .prō-.tē-'nō-səs, -tē-ə- n, pl -o·ses -.sēz or -o·sis·es the accumulation of abnormal amounts of protein in bodily tissues see PULMONARY ALVEOLAR PROTEINOSIS

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pro·tein·o·sis (pro″tēn-oґsis) the accumulation of excess protein in the tissues.

Medical dictionary. 2011.