Syndrome, Launois-Bensaude
A disorder characterized by painless symmetrical diffuse deposits of fat beneath the skin of the neck, upper trunk, arms and legs. The condition is thought to be genetic although its exact mode of inheritance is uncertain; it may be a mitochondrial DNA disease. It frequently appears in association with alcoholic liver disease, macrocytic anemia ("low blood" with big red blood cells) and peripheral neuropathy (disease of the peripheral nervous system, as opposed to the brain and spinal cord). The peripheral neuropathy has often been laid to alcoholism, but the neuropathy is likely an integral part of the syndrome. This disorder affects mainly men and is more frequent in the Mediterranean area. It has been suggested that the distribution of fat in this disease resembles that of a pre-Roman (6th century BC) Italic statue called the Capestrano warrior discovered in the Abruzzi region of Italy. The syndrome is also known as multiple symmetrical lipomatosis, cephalothoracic lipodystrophy, and Madelung disease. It was called 'fat neck' (Fetthals) by Madelung in 1888.

Medical dictionary. 2011.

Look at other dictionaries:

  • Launois-Bensaude syndrome — A disorder characterized by painless symmetrical diffuse deposits of fat beneath the skin of the neck, upper trunk, arms and legs. The condition is thought to be genetic although its exact mode of inheritance is uncertain; it may be a… …   Medical dictionary

  • syndrome — The aggregate of symptoms and signs associated with any morbid process, and constituting together the picture of the disease. SEE ALSO: disease. [G. s., a running together, tumultuous concourse; (in med.) a concurrence of symptoms, fr. syn,… …   Medical dictionary

  • Launois — Pierre E., French physician, 1856–1914. See L. Cléret syndrome, L. Bensaude syndrome …   Medical dictionary

  • Raoul Bensaude — (1866 October 25, 1938) was a French physician who practiced medicine in Paris. He is known for his work with Emile Charles Achard (1860 1944) involving the description of paratyphoid fever and isolation of the bacillus, Salmonella paratyphi B .… …   Wikipedia

  • Pierre-Emile Launois — (1856 March 18, 1914) was a French physican who was a native of the department of Marne. He studied in Reims and Paris, where in 1885 he earned his medical doctorate. He became médecin des hôpitaux in 1895, and professeur agrégé of histology in… …   Wikipedia

  • Liste der Syndrome — Diese Seite listet in alphabetischer Reihenfolge und ohne Anspruch auf Vollständigkeit Syndrome und Komplexe aus unterschiedlichen medizinischen Fachgebieten auf. Bitte nur Verweise auf den tatsächlichen Titel des Beitrags und keine… …   Deutsch Wikipedia

  • Liste Des Maladies Rares — Liste des maladies commençant par une lettre Mise en garde médicale Maladie rare Liste des maladies rares Commençant par un chiffre Commençant par une lettre …   Wikipédia en Français

  • Liste de maladies rares — Cette page liste des maladies rares. Sommaire : Haut A B C D E F G H I J K L M N O P Q R S T U V W X Y Z 0 9 A Aagenaes, syndrome d …   Wikipédia en Français

  • Liste des maladies commençant par une lettre — Mise en garde médicale Maladie rare Liste des maladies rares Commençant par un chiffre Commençant par une lettre …   Wikipédia en Français

  • Liste des maladies rares — Liste des maladies commençant par une lettre Mise en garde médicale Maladie rare Liste des maladies rares Commençant par un chiffre Commençant par une lettre …   Wikipédia en Français

Share the article and excerpts

Direct link
Do a right-click on the link above
and select “Copy Link”